Gossing L.,Catholic University of Leuven |
Staudt J.P.,Service de chirurgie thoracique |
Cvilic S.,Service de radiotherapie |
Venet C.,Service de radiologie |
And 2 more authors.
Louvain Medical | Year: 2011
Thoracic synovial sarcoma is an uncommon mesenchymal tumor requiring a systematic diagnostic approach. Pathological and cytogenetical features allow a defi nitive diagnosis. Therapeutic management includes surgical resection and adjuvant radiotherapy in case of the absence of metastasis. We report the case of a young 18-year-old woman who presented with thoracic pain and progressive dyspnea. Thoracic imaging revealed a voluminous pleural basal tumoral lesion. A right voluminous synovial sarcoma was diagnosed, confirmed by detecting a translocation of the gene SSX1/SSX2 and the gene SYT. The patient benefi ted from a complete surgical resection and an adjuvant radiotherapy was performed. Diagnostic and therapeutic management has been reviewed.